definitionRare disorder characterized by proliferation of fibroblasts and excessive deposition of acid mucopolysaccharides in the skin. Numerous lichenoid papules are formed which may coalesce together to form generalized plaques, causing thickening and hardening of the skin. Cardiovascular abnormalities as well as neurologic involvement may occur. | synonymsLichen Myxoedematosus, Papular Mucinosis, Mucinosis Papulosa seu Lichenoides, Myxoderma Papulosum, Lichen Fibromucinodosis |
UMLSLichen myxedematosus, Lichen myxoedematosus, Lichenoid myxedema, Mucinosis papular, Papular mucinosis, Scleromyxedema, Scleromyxoedema |
|
|