definitionDermatosis occurring either as an isolated genetic trait with autosomal dominant inheritance or together with connective tissue disorders such as Ehlers-Danlos syndrome, Marfan’s syndrome and osteogenesis imperfecta. In this dermatosis, transepidermal extrusion of elastic material occurs, frequently peri- or transfollicularly. The disorder presents with annular, circular, serpiginous, ridged lesions consisting of narrow, hard, keratotic or verruciform reddish papules. The lesions show a tendency to peripheral progression and central healing. The neck, the cheeks, and the extremities are particularly involved. Perforating Elastoma mainly begins in youth. | synonymsPerforating Elastoma, Elastosis Perforans Serpiginosa, Elastosis Intrapapillare Perforans Verucciforme, Perforating Serpiginous Elastosis |
UMLSDisease, Lutz-Miescher, Elastoma, Miescher's, Elastosis perforan serpiginosa, Elastosis perforans serpiginosa, Elastosis, perforans serpiginosa, Keratosis follicul serpiginosa, Keratosis follicularis serpiginosa, LUTZ-MIESCHER DISEASE, Miescher's elastoma, Perforat serpiginous elastosis, Perforating elastoma, PERFORATING ELASTOSIS, Perforating serpiginous elastosis |
|
|