DefinitionRare histiocytosis belonging to Class II histiocytoses (the accumulating cells are mononuclear phagocytes other than Langerhans cells). Lesions usually appear at the end of the first year of life, presenting as erythematous papules, nodules and plaques which develop on the cheeks, forehead, earlobes and neck. They may spread to the trunk and upper limbs, gradually turning to reddish-brown. Visceral involvement has not been described. The disease is self-limiting. | SynonymeBenigne Histiozytose des Kopfes |
Bilder | 1 Bild für diese Diagnose |
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