definition
A slowly progressive autosomal dominant disorder of keratinization characterized by pinkish-to-tan papules that coalesce to form plaques. These lesions become darker over time and commonly fuse, forming papillomatous and warty malodorous growths.
synonyms
Keratosis Pilaris, Keratosis Follicularis, Lichen Pilaris
UMLS
Darier Disease, Dariers Disease, Darier's Disease, Darier-White disease, Disease, Darier, Disease, Darier's, Dyskeratosis follicularis, Dyskeratosis, follicularis, Keratosis Follicularis, Keratosis, follicularis, PSOROSPERMOSIS, FOLLICULARIS, WHITE-DARIER DISEASE