search string

Search

by localization

 

Melanosis Neurocutanea

definition

Rare condition characterized by extensive congenital hairy nevocytic nevi, often in the bathing trunk region, a dense scattering of smaller, pigmented nevocytic nevi, especially on the palms and soles, and similar aggregations of pigment-forming naevus cells in the meninges, brain, and spinal cord. Complications arise from the development of an obstructive internal hydrocephalus. A metastasising melanoma may also arise in the skin or CNS, accounting for the poor prognosis of the disorder.

synonyms

Melanosis Neurocutanea, Melanoblastosis Neurocutanea Touraine, Neurocutaneous Melanosis

images

2 images found for this diagnose localisation: shoulder region, diagnosis: Melanosis Neurocutanea localisation: abdomen, upper leg, diagnosis: Melanosis Neurocutanea