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Urticaria Pigmentosa

definition

The most common form of mastocytosis. It occurs primarily in children and is characterized by multiple persistent small, reddish-brown, hyperpigmented, pruritic macules and papules due to an increased number of mast cells. They are located most commonly on the trunk, but are also seen on the extremities, head, and neck. Friction leads to the release of histamine and wheal formation in the lesions (Darier’s sign), sometimes with blistering. Involvement of internal organs may occur.

synonyms

Urticaria Pigmentosa

UMLS

Localized cutaneous mastocytosis, NOS, Urticaria Pigmentosa, Urticaria pigmentosa, NOS, Urticaria, pigmentosa

Images

23 images found for this diagnose
localisation: back, diagnosis: Urticaria Pigmentosa localisation: abdomen, upper leg, diagnosis: Urticaria Pigmentosa localisation: arms, legs, diagnosis: Urticaria Pigmentosa localisation: face, diagnosis: Urticaria Pigmentosa localisation: sole, diagnosis: Urticaria Pigmentosa localisation: face, diagnosis: Urticaria Pigmentosa diagnosis: Urticaria Pigmentosa diagnosis: Urticaria Pigmentosa diagnosis: Urticaria Pigmentosa diagnosis: Urticaria Pigmentosa diagnosis: Urticaria Pigmentosa diagnosis: Urticaria Pigmentosa diagnosis: Urticaria Pigmentosa diagnosis: Urticaria Pigmentosa diagnosis: Urticaria Pigmentosa diagnosis: Urticaria Pigmentosa diagnosis: Urticaria Pigmentosa diagnosis: Urticaria Pigmentosa diagnosis: Urticaria Pigmentosa diagnosis: Urticaria Pigmentosa diagnosis: Urticaria Pigmentosa diagnosis: Urticaria Pigmentosa diagnosis: Urticaria Pigmentosa