Suchbegriff

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nach Körperregion

Granulomatosis Wegener

Definition

A multisystem disease chiefly affecting males, characterized by necrotizing granulomatous vasculitis involving the upper and lower respiratory tracts, glomerulonephritis, and variable degrees of systemic, small vessel vasculitis, which is generally considered to represent an aberrant hypersensitivity reaction to an unknown antigen. (Dorland, 27th ed)

Synonyme

Granulomatosis Wegener, Wegener-Granulomatose, Maligne granulomatöse Angiitis, Rhinogene Granulomatose, Wegener-Klinger-Churg-Strauss-Syndrom

UMLS

WEGENER-GRANULOMATOSE